Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II)

By Fujita Eriko   Kouroku Yoriko   Kumagai Hiromichi   Misutani Akifumi   Matsuda Chie   Hayashi Yukiko K.   Momoi Takashi  

Human Molecular Genetics, Vol. 16, Iss. 6, 2007-03 ,pp. : 618-629

Oxford University Press

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Broad activation of the ubiquitin–proteasome system by Parkin is critical for mitophagy

By Chan Nickie C.   Salazar Anna M.   Pham Anh H.   Sweredoski Michael J.   Kolawa Natalie J.   Graham Robert L.J.   Hess Sonja   Chan David C.  

Human Molecular Genetics, Vol. 20, Iss. 9, 2011-05 ,pp. : 1726-1737

Oxford University Press

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Blocking acid-sensing ion channel 1 alleviates Huntington's disease pathology via an ubiquitin-proteasome system-dependent mechanism

By Wong Hon Kit   Bauer Peter O.   Kurosawa Masaru   Goswami Anand   Washizu Chika   Machida Yoko   Tosaki Asako   Yamada Mizuki   Knpfel Thomas   Nakamura Takemichi   Nukina Nobuyuki  

Human Molecular Genetics, Vol. 17, Iss. 20, 2008-10 ,pp. : 3223-3235

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Functional alterations of the ubiquitin-proteasome system in motor neurons of a mouse model of familial amyotrophic lateral sclerosis

By Cheroni Cristina   Marino Marianna   Tortarolo Massimo   Veglianese Pietro   De Biasi Silvia   Fontana Elena   Zuccarello Laura Vitellaro   Maynard Christa J.   Dantuma Nico P.   Bendotti Caterina  

Human Molecular Genetics, Vol. 18, Iss. 1, 2009-01 ,pp. : 82-96

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Neuronal dysfunction in a polyglutamine disease model occurs in the absence of ubiquitin–proteasome system impairment and inversely correlates with the degree of nuclear inclusion formation

By Bowman Aaron B.  

Human Molecular Genetics, Vol. 14, Iss. 5, 2005-03 ,pp. : 679-691

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