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Human Molecular Genetics, Vol. 13, Iss. 18, 2004-09 ,pp. : 2031-2042

Oxford University Press

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Selective vulnerability of motor neurons and dissociation of pre- and post-synaptic pathology at the neuromuscular junction in mouse models of spinal muscular atrophy

By Murray Lyndsay M.   Comley Laura H.   Thomson Derek   Parkinson Nick   Talbot Kevin   Gillingwater Thomas H.  

Human Molecular Genetics, Vol. 17, Iss. 7, 2008-04 ,pp. : 949-962

Oxford University Press

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A mouse model of spinal and bulbar muscular atrophy

By O'Bryan M.K.  

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Restoration of SMN to Emx-1 expressing cortical neurons is not sufficient to provide benefit to a severe mouse model of Spinal Muscular Atrophy

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Transgenic Research, Vol. 22, Iss. 5, 2013-10 ,pp. : 1029-1036

Springer Publishing Company

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Neurofilament accumulation at the motor endplate and lack of axonal sprouting in a spinal muscular atrophy mouse model

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