Combined saposin C and D deficiencies in mice lead to a neuronopathic phenotype, glucosylceramide and -hydroxy ceramide accumulation, and altered prosaposin trafficking

Author： Sun Ying   Witte David P.   Zamzow Matt   Ran Huimin   Quinn Brian   Matsuda Junko   Grabowski Gregory A.  

Publisher： Oxford University Press

ISSN： 1460-2083

Source： Human Molecular Genetics, Vol.16, Iss.8, 2007-04, pp. : 957-971

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