Phytanoyl-CoA Hydroxylase Is Present in Human Liver, Located in Peroxisomes, and Deficient in Zellweger Syndrome: Direct, Unequivocal Evidence for the New, Revised Pathway of Phytanic Acid alpha-Oxidation in Humans

Author： Jansen G.A.   Mihalik S.J.   Watkins P.A.   Moser H.W.   Jakobs C.   denis S.   Wanders R.J.A.  

Publisher： Elsevier

ISSN： 0006-291X

Source： Biochemical and Biophysical Research Communications, Vol.229, Iss.1, 1996-12, pp. : 205-210

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