Morphological Alterations and Cell Death Provoked by the Branched-Chain α-Amino Acids Accumulating in Maple Syrup Urine Disease in Astrocytes from Rat Cerebral Cortex

By Funchal Cláudia   Gottfried Carmem   Almeida Lúcia   Santos André   Wajner Moacir   Pessoa-Pureur Regina  

Cellular and Molecular Neurobiology, Vol. 25, Iss. 5, 2005-08 ,pp. : 851-867

Springer Publishing Company

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Creatine and Antioxidant Treatment Prevent the Inhibition of Creatine Kinase Activity and the Morphological Alterations of C6 Glioma Cells Induced by the Branched-Chain α-Keto Acids Accumulating in Maple Syrup Urine Disease

By Funchal Cláudia   Schuck Patrícia   Santos André   Jacques-Silva Maria   Gottfried Carmem   Pessoa-Pureur Regina   Wajner Moacir  

Cellular and Molecular Neurobiology, Vol. 26, Iss. 1, 2006-02 ,pp. : 67-79

Springer Publishing Company

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Induction of oxidative stress in rat brain by the metabolites accumulating in maple syrup urine disease

By Bridi R.   Araldi J.   Sgarbi M.B.   Testa C.G.   Durigon K.   Wajner M.   Dutra-Filho C.S.  

International Journal of Developmental Neuroscience, Vol. 21, Iss. 6, 2003-10 ,pp. : 327-332

Elsevier

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In vitro effects of d-2-hydroxyglutaric acid on glutamate binding, uptake and release in cerebral cortex of rats

By Junqueira D.   Brusque A.M.   Porciuncula L.O.   Rotta L.N.   Frizzo M.E.S.   Wyse A.T.S.   Wannmacher C.M.D.   Souza D.O.   Wajner M.  

Journal of the Neurological Sciences, Vol. 217, Iss. 2, 2004-02 ,pp. : 189-194

Elsevier

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Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease

By Zinnanti William J.  

Brain, Vol. 132, Iss. 4, 2009-04 ,pp. : 903-918

Oxford University Press

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