Moyamoya Disease in Children with Congenital Dwarfing Conditions

Publisher: Karger

E-ISSN: 1423-0305|46|5|373-380

ISSN: 1016-2291

Source: Pediatric Neurosurgery, Vol.46, Iss.5, 2011-03, pp. : 373-380

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Abstract

Congenital dwarfisms can be associated with a variety of vascular anomalies. Here, we describe 2 patients with congenital dwarfisms who presented with moyamoya syndrome and underwent indirect intracranial revascularization. The pathogenesis of moyamoya syndrome in this population is not well understood, but it is a major cause of stroke and early death in these patients, making their timely diagnosis and management critical.