Mitochondrial iron detoxification is a primary function of frataxin that limits oxidative damage and preserves cell longevity

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Human Molecular Genetics, Vol. 15, Iss. 3, 2006-02 ,pp. : 467-479

Oxford University Press

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Friedreich ataxia: the oxidative stress paradox

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Human Molecular Genetics, Vol. 14, Iss. 4, 2005-02 ,pp. : 463-474

Oxford University Press

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Assembly and iron-binding properties of human frataxin, the protein deficient in Friedreich ataxia

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Human Molecular Genetics, Vol. 11, Iss. 3, 2002-02 ,pp. : 217-227

Oxford University Press

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Iron-dependent regulation of frataxin expression: implications for treatment of Friedreich ataxia

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Oxford University Press

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Mutation of a putative mitochondrial iron transporter gene ( ABC7 ) in X-linked sideroblastic anemia and ataxia (XLSA/A)

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Human Molecular Genetics, Vol. 8, Iss. 5, 1999-05 ,pp. : 743-749

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