Interferon gamma upregulates frataxin and corrects the functional deficits in a Friedreich ataxia model

By Tomassini Barbara   Arcuri Gaetano   Fortuni Silvia   Sandi Chiranjeevi   Ezzatizadeh Vahid   Casali Carlo   Condò Ivano   Malisan Florence   Al-Mahdawi Sahar   Pook Mark   Testi Roberto  

Human Molecular Genetics, Vol. 21, Iss. 13, 2012-07 ,pp. : 2855-2861

Oxford University Press

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Friedreich ataxia: the oxidative stress paradox

By Seznec Hervé  

Human Molecular Genetics, Vol. 14, Iss. 4, 2005-02 ,pp. : 463-474

Oxford University Press

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A TAT–Frataxin fusion protein increases lifespan and cardiac function in a conditional Friedreich's ataxia mouse model

By Vyas Piyush M.   Tomamichel Wendy J.   Pride P. Melanie   Babbey Clifford M.   Wang Qiujuan   Mercier Jennifer   Martin Elizabeth M.   Payne R. Mark  

Human Molecular Genetics, Vol. 21, Iss. 6, 2012-03 ,pp. : 1230-1247

Oxford University Press

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A cellular model for Friedreich Ataxia reveals small-molecule glutathione peroxidase mimetics as novel treatment strategy

By Jauslin M.L.  

Human Molecular Genetics, Vol. 11, Iss. 24, 2002-09 ,pp. : 3055-3063

Oxford University Press

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Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia

By Seznec Hervé   Simon Delphine   Monassier Laurent   Criqui-Filipe Paola   Gansmuller Anne   Rustin Pierre   Koenig Michel   Puccio Hélène  

Human Molecular Genetics, Vol. 13, Iss. 10, 2004-05 ,pp. : 1017-1024

Oxford University Press

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