Oxidative stress causes abnormal accumulation of familial amyotrophic lateral sclerosis-related mutant SOD1 in transgenic Caenorhabditis elegans

By Ishii N.   Oeda T.   Shimohama S.   Kitagawa N.   Kohno R.   Imura T.   Shibasaki H.  

Human Molecular Genetics, Vol. 10, Iss. 19, 2001-09 ,pp. : 2013-2023

Oxford University Press

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Functional alterations of the ubiquitin-proteasome system in motor neurons of a mouse model of familial amyotrophic lateral sclerosis

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Human Molecular Genetics, Vol. 18, Iss. 1, 2009-01 ,pp. : 82-96

Oxford University Press

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Variation in the biochemical/biophysical properties of mutant superoxide dismutase 1 enzymes and the rate of disease progression in familial amyotrophic lateral sclerosis kindreds

By Ratovitski Tamara  

Human Molecular Genetics, Vol. 8, Iss. 8, 1999-08 ,pp. : 1451-1460

Oxford University Press

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Calcium-permeable AMPA receptors promote misfolding of mutant SOD1 protein and development of amyotrophic lateral sclerosis in a transgenic mouse model

By Tateno Minako  

Human Molecular Genetics, Vol. 13, Iss. 19, 2004-10 ,pp. : 2183-2196

Oxford University Press

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The small heat shock protein B8 (HspB8) promotes autophagic removal of misfolded proteins involved in amyotrophic lateral sclerosis (ALS)

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Human Molecular Genetics, Vol. 19, Iss. 17, 2010-09 ,pp. : 3440-3456

Oxford University Press

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