A new mechanism for mtDNA pathogenesis: impairment of post-transcriptional maturation leads to severe depletion of mitochondrial tRNA Ser(UCN) caused by T7512C and G7497A point mutations

Author： Möllers Myriam   Maniura-Weber Katharina   Kiseljakovic Emina   Bust Maria   Hayrapetyan Armine   Jaksch Michaela   Helm Mark   Wiesner Rudolf J.   von Kleist-Retzow Jürgen-Christoph  

Publisher： Oxford University Press

ISSN： 1362-4962

Source： Nucleic Acids Research, Vol.33, Iss.17, 2005-01, pp. : 5647-5658

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