The GAA triplet-repeat is unstable in the context of the human FXN locus and displays age-dependent expansions in cerebellum and DRG in a transgenic mouse model

Author： Clark Rhonda   De Biase Irene   Malykhina Anna   Al-Mahdawi Sahar   Pook Mark   Bidichandani Sanjay  

Publisher： Springer Publishing Company

ISSN： 0340-6717

Source： Human Genetics, Vol.120, Iss.5, 2007-01, pp. : 633-640

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