Adenovirus-mediated expression of mutant DRPLA proteins with expanded polyglutamine stretches in neuronally differentiated PC12 cells. Preferential intranuclear aggregate formation and apoptosis

Author： Sato Aki   Shimohata Takayoshi   Koide Reiji   Takano Hiroki   Sato Toshiya   Oyake Mutsuo   Igarashi Shuichi   Tanaka Keiko   Inuzuka Takashi   Nawa Hiroyuki   Tsuji Shoji   Koide R.   Nagafuchi S.   Takano K.   La Spada A.R.   Orr H.T.   Sanpei K.   Pulst S.M.   Imbert G.   Kawaguchi Y.   Zhuchenko O.   Lindblad K.   Yazawa I.   Trottier Y.   Servadio A.   Onodera O.   Burright E.N.   Ikeda H.   Igarashi S.   Martindale D.   Cooper J.K.   Lunkes A.   Paulson H.L.   Davies S.W.   Hayashi Y.   Holmberg M.   Skinner P.J.   Li M.   Naito H.   Takahashi H.   Miyake S.   Klement I.A.   Saudou F.   Walter P.   Miyashita T.   Kanegae Y.   Precious B.   Hierholzer J.C.   Greene L.A.  

Publisher： Oxford University Press

ISSN： 1460-2083

Source： Human Molecular Genetics, Vol.8, Iss.6, 1999-06, pp. : 997-1006

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