Molecular and phenotypic characterization of a mouse model of oculopharyngeal muscular dystrophy reveals severe muscular atrophy restricted to fast glycolytic fibres

Author： Trollet Capucine   Anvar Seyed Yahya   Venema Andrea   Hargreaves Iain P.   Foster Keith   Vignaud Alban   Ferry Arnaud   Negroni Elisa   Hourde Christophe   Baraibar Martin A.   't Hoen Peter A.C.   Davies Janet E.   Rubinsztein David C.   Heales Simon J.   Mouly Vincent   van der Maarel Silvre M.   Butler-Browne Gillian   Raz Vered   Dickson George  

Publisher： Oxford University Press

ISSN： 1460-2083

Source： Human Molecular Genetics, Vol.19, Iss.11, 2010-06, pp. : 2191-2207

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