Inhibiting the ubiquitinproteasome system leads to preferential accumulation of toxic N-terminal mutant huntingtin fragments

Author： Li Xiang   Wang Chuan-En   Huang Shanshan   Xu Xingshun   Li Xiao-Jiang   Li He   Li Shihua  

Publisher： Oxford University Press

ISSN： 1460-2083

Source： Human Molecular Genetics, Vol.19, Iss.12, 2010-06, pp. : 2445-2455

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